Hereditary fructose intolerance is a very rare disease.

(Intolerance = intolerance, also hereditary fructose malabsorption)

digestive problems arise such as abdominal pain (abdominal discomfort), gas, diarrhea or nausea.

Here, fructose (fruit sugar) is not tolerated.

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Fructose is a simple sugar (monosaccharide) & occurs mainly in fruits, fruit juices but also in many other industrially manufactured products (check the list of ingredients).

It is a congenital genetic defect. Patients have to go without fructose-containing foods for life. As soon as the person concerned follows a fructose-free diet and also refrains from other sweeteners that can be converted to fructose or contain it, the symptoms recede quickly. Infants with hereditary fructose intolerance usually have no problems as long as they are still breastfed (breast milk does not contain fructose). However, as soon as breastfeeding is no longer exclusively and complementary foods are introduced, it is important to monitor the compatibility of foods.

Tip for the 1st year of life:

In the first year of life, the child should not eat fruit or vegetables. To avoid a vitamin deficiency, the child is given dietary supplements. Ready-made porridges should be checked (list of ingredients), as they can contain fructose. It is better to prepare porridges yourself

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Tablets also often contain sorbitol. In the case of hereditary fructose intolerance, those affected should therefore carefully study the package insert for drugs and food supplements and check what the tablets are made of. It should be noted that prescribed medication should not be discontinued without authorization, but only in consultation with the doctor. Your doctor can help find alternatives.

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Can the disease go undetected?

If the introduction of complementary foods contains hardly any fructose in infants (contrary to the recommendations), the disease may go undetected. Even small diet errors lead to malaise. These children develop an aversion (aversion) to fruit and all sweets, avoid these high-fructose foods and then typically show no symptoms. Damage to the liver and kidneys only occurs when too much fructose is consumed.

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Diagnosis: Gold standard : H2 breath test.

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Please also have a test for sorbitol intolerance carried out immediately.

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Why is nutritional therapy important?

Nutritional therapy supports you in relieving and resolving your complaints.

The aim is to supply all of the fatty acids, micronutrients (vitamins and minerals) that are important to you, energy and protein in the measure that your body is optimally supplied with. For this purpose, foods that promote inflammation are specifically avoided and plenty of anti-inflammatory foods are consumed. Weight reduction is recommended if you are overweight / obese. An anti-inflammatory diet can improve the state of health.

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Classification of your weight - definition and classification of weight in relation to height.

Special percentile curves apply to children and adolescents; the BMI cannot simply be used here.

BMI and interpretation: BMI: body mass index. Formula: Body weight in kg : (body height in m) 2

Underweight: <18.5

Normal weight: 18.5 - 24.9

Overweight = pre-obesity: 25-29.9

Obesity grade I: 30 - 34.9

Obesity grade II: 35-39.9

Obesity grade III:> 40 = per magna

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Nutritional therapy

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• Lifelong diet therapy with a maximum of 0.5-2 g fructose per day is tolerable (= strict fructose-free diet)

• Which foods are fructose-free?

• Must fructose from grain products also be avoided?

• Which foods do I have to "do without" which ones can I eat without hesitation?

• Anti-inflammatory nutrition as a basis, individually tailored to you

• Holistic therapy - do you have any comorbidities that need to be taken into account during the consultation?

• Overall fat selection, how should it be designed

• How many animal foods (e.g. meat products, milk and dairy products, cheese, fish products, eggs) are recommended?

• What do I have to look out for when choosing animal foods?

• How can I counteract inflammatory processes through diet?

• Body weight: Weight reduction is recommended if you are overweight / obese.

• In the case of insulin resistance and lipid metabolism disorders, also treat them with nutritional therapy

• Avoid micronutrient deficiencies and mineral deficiencies & possibly counteract them with nutrient preparations

• Prevent protein deficiency

• Which nutrients do I need in which ratio?

• Get enough fiber (> 30 g / day) through natural foods, possibly fiber substitution

• Sufficient fluid: total fluid per day: 30 - 35 ml per kg body weight and day. Attention, this is not just a drinking liquid. The liquid from food (approx. 500 - 800 ml) must still be subtracted from this, so that an amount of approx. 1.3 - 2 l of drinking liquid is created.

• add valuable anti-carcinogenic (anti-cancer) secondary plant substances

• A selection of foods tailored to your needs with cooking and technical information (for breakfast, snacks, lunch, dinner)

• Do you like to eat your warm meal in the evening? I am happy to cater to your individual situation and we will create a plan on how you can implement your wholesome diet into your everyday life.

• which oils are good for me? What should I watch out for in relation to the anti-inflammatory diet?

• How much fat spread (butter / margarine / vegetable fat) can I use and which products are recommended?

• Get enough Omgea-3 fatty acids and essential fatty acids

• How can I boost and support my metabolism with natural foods?

• Coordinate sensible meal frequency for your individual case - meal allocation

• Define the desired weight stabilization / normalization & the estimated period for this

• what should be considered with beverages and alcoholic beverages?

• How does exercise affect your body and thus also your diet?

• Avoid blood sugar fluctuations

• Sweetening foods - sweeteners, glucose, fructose, sugar and sugar substitutes, what can I use and in what quantities? How high is the respective sweetness of the different products?

• what should be considered when baking and cooking?

• what are cheap snacks / main meals

• Eating out - what should you watch out for?

• Vacation, boat trip or hospital stay, what should be considered?

• Flatulence, bloating, diarrhea, constipation, vomiting, heartburn, loss of appetite, pain related to eating, what can I do about it?

• Daily plans as an example for practical implementation in everyday life

• Enjoyment training

• Optimizing your eating situation

• long-term maintenance of a jointly defined weight

• Strengthen the stomach and intestines with natural foods

• Additional therapy options

• Dietetic products in support of nutritional therapy

• Food supplements - under certain circumstances, a supplement can be useful

• and other topics

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Any questions? I look forward to your call or email. To contact form

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Assistance:

• KISS self-help groups

• Self-help network

• Working group dietetics in allergology e. V.

• German Allergy and Asthma Association

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